MRCEM Notes

Churg-Strauss syndrome

Churg-Strauss syndrome is an ANCA associated small-medium vessel vasculitis.

Features
  • asthma
  • blood eosinophilia (e.g. > 10%)
  • paranasal sinusitis
  • mononeuritis multiplex
  • pANCA positive in 60%

Comparison of granulomatosis with polyangiitis and Churg-Strauss syndrome

Leukotriene receptor antagonists may precipitate the disease
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