MRCEM Notes

Cleft lip and palate

Cleft lip and palate affect around 1 in every 1,000 babies. They are the most common congenital deformity affecting the orofacial structures. Whilst they may be an isolated developmental malformation they are also a recognised component of more than 200 birth defects.

The commonest variants are:
  • isolated cleft lip (15%)
  • isolated cleft palate (40%)
  • combined cleft lip and palate (45%)

Pathophysiology
  • polygenic inheritance
  • maternal antiepileptic use increases risk
  • cleft lip results from failure of the fronto-nasal and maxillary processes to fuse
  • cleft palate results from failure of the palatine processes and the nasal septum to fuse

Problems
  • feeding: orthodontic devices may be helpful
  • speech: with speech therapy 75% of children develop normal speech
  • increased risk of otitis media for cleft palate babies

Management
  • cleft lip is repaired earlier than cleft palate, with practices varying from repair in the first week of life to three months
  • cleft palates are typically repaired between 6-12 months of age
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